What is Hemophilia?

Hemophilia is a genetic disorder due to the absence of the anti-hemophilic factor.

Clinical Features of Hemophilia

1. After an injury, bleeding occurs for hours or days depending on whether it is a mild disease or a severe disease.
2. Large collections of partially coagulated blood puts pressure on adjoining organs causing muscle cell death, venous congestion or damage to nerves. These collections can become calcified.
3. Typically a hemophiliac patient presents with pain followed by swelling in a weight-bearing joint
like the hip, knee or ankle. Presence of blood in the joint causes inflammation of the synovium. Repeated bleeding, erodes joints and causes osteoarthritis.
4. Blood in the urine is also common.

Management of Hemophilia

Patient to be under the care of a physician.

Complications of Hemophilia

AIDS, Hepatitis B due to transfusions with untested blood.

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